Partial Anomalous Pulmonary Venous Connections

Surgical Management

José Fragata, Manuel Magalhães, Luis Baquero, Conceição Trigo, Fátima Pinto, Isabel Fragata

Research output: Contribution to journalArticle

5 Citations (Scopus)

Abstract

Partial anomalous pulmonary venous connections (PAPVCs) are a heterogeneous group of congenital heart lesions in which at least one pulmonary vein will drain into the systemic venous system. The consequences are a variable left-to-right hemodynamic shunt and more rarely pulmonary artery hypertension. Often, PAPVC occurs in association with other congenital cardiac malformations. Surgical correction is most often advisable and is generally straightforward and simple to achieve. Historically, some repairs have included incision across the junction of the superior vena cava with the right atrium, which can lead to late arrhythmias. The Warden technique avoids incision across the atriocaval junction. Neonates and infants with Scimitar syndrome represent the most challenging subset of patients with PAPVC.

Original languageEnglish
Pages (from-to)44-49
Number of pages6
JournalWorld Journal for Pediatric and Congenital Heart Surgery
Volume4
Issue number1
DOIs
Publication statusPublished - 2013

Fingerprint

Lung
Scimitar Syndrome
Superior Vena Cava
Pulmonary Veins
Heart Atria
Pulmonary Hypertension
Pulmonary Artery
Cardiac Arrhythmias
Hemodynamics
Newborn Infant

Keywords

  • anomalous
  • pulmonary
  • return
  • veins

Cite this

Fragata, José ; Magalhães, Manuel ; Baquero, Luis ; Trigo, Conceição ; Pinto, Fátima ; Fragata, Isabel. / Partial Anomalous Pulmonary Venous Connections : Surgical Management. In: World Journal for Pediatric and Congenital Heart Surgery. 2013 ; Vol. 4, No. 1. pp. 44-49.
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Partial Anomalous Pulmonary Venous Connections : Surgical Management. / Fragata, José; Magalhães, Manuel; Baquero, Luis; Trigo, Conceição; Pinto, Fátima; Fragata, Isabel.

In: World Journal for Pediatric and Congenital Heart Surgery, Vol. 4, No. 1, 2013, p. 44-49.

Research output: Contribution to journalArticle

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