Fibropolycystic Liver Diseases

Carlos Bilreiro, Inês Santiago

Research output: Chapter in Book/Report/Conference proceedingChapter

Abstract

Fibropolycystic liver diseases are a group of congenital disorders with a common origin in ductal plate developmental abnormalities and varied fenotypes. They include the simple hepatic cysts, Caroli disease and syndrome, polycystic liver diseases, congenital hepatic fibrosis and biliary hamartomas. In this chapter, we first discuss the embryologic developent of the normal ductal plate and of the multiple ductal plate abnormalities. Then, we individually address the various fibropolycystic liver diseases with respect to their epidemiology, clinical features and therapeutic management, with a special emphasis on the description and illustration of their imaging findings.

Original languageEnglish
Title of host publicationMedical Radiology
PublisherSpringer Science and Business Media Deutschland GmbH
Pages225-240
Number of pages16
DOIs
Publication statusPublished - 2021

Publication series

NameMedical Radiology
ISSN (Print)0942-5373
ISSN (Electronic)2197-4187

Fingerprint Dive into the research topics of 'Fibropolycystic Liver Diseases'. Together they form a unique fingerprint.

  • Cite this

    Bilreiro, C., & Santiago, I. (2021). Fibropolycystic Liver Diseases. In Medical Radiology (pp. 225-240). (Medical Radiology). Springer Science and Business Media Deutschland GmbH. https://doi.org/10.1007/978-3-030-38983-3_11