Fasceíte eosinofílica e aplasia medular

Sandra Falcão; Ana F. Mourão; Célia Ribeiro; Teresa L. Pinto; Margarida Mateus; Paula Araújo; Patrícia Nero; J. Bravo Pimentão; J. Cunha Branco

Fasceíte eosinofílica e aplasia medular

Translated title of the contribution: Eosinophilic fasciitis and aplastic anemia

Sandra Falcão, Ana F. Mourão, Célia Ribeiro, Teresa L. Pinto, Margarida Mateus, Paula Araújo, Patrícia Nero, J. Bravo Pimentão, J. Cunha Branco

NOVA Medical School|Faculdade de Ciências Médicas (NMS|FCM)

Research output: Contribution to journal › Article › peer-review

3 Citations (Scopus)

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Abstract

Eosinophilic fasciitis is a rare rheumatic condition characterized by inflammatory thickening of the skin and fascia, peripheral eosinophilia, elevated erythrocyte sedimentation rate and hypergammaglobulinemia. Internal organ involvement is uncommon. It is often difficult to diagnose eosinophilic fasciitis and its course may be variable. Glucocorticoids are most commonly used in the treatment but in many cases they are ineffective, requiring combined immunosuppressive treatment. Several cases of eosinophilic fasciitis and serious haematological disorders such as immune thrombocytopenia, Hodgkin's disease and aplastic anaemia have been described. The authors report an atypical severe case of eosinophilic fasciitis complicated by aplastic anaemia non responsive to treatment.

Translated title of the contribution	Eosinophilic fasciitis and aplastic anemia
Original language	Portuguese
Pages (from-to)	120-126
Number of pages	7
Journal	Acta Reumatologica Portuguesa
Volume	34
Issue number	1
Publication status	Published - Jan 2009

Keywords

Aplastic anemia
Eosinophilic fasciitis

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Cite this

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title = "Fasce{\'i}te eosinof{\'i}lica e aplasia medular",

abstract = "Eosinophilic fasciitis is a rare rheumatic condition characterized by inflammatory thickening of the skin and fascia, peripheral eosinophilia, elevated erythrocyte sedimentation rate and hypergammaglobulinemia. Internal organ involvement is uncommon. It is often difficult to diagnose eosinophilic fasciitis and its course may be variable. Glucocorticoids are most commonly used in the treatment but in many cases they are ineffective, requiring combined immunosuppressive treatment. Several cases of eosinophilic fasciitis and serious haematological disorders such as immune thrombocytopenia, Hodgkin's disease and aplastic anaemia have been described. The authors report an atypical severe case of eosinophilic fasciitis complicated by aplastic anaemia non responsive to treatment.",

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language = "Portuguese",

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T1 - Fasceíte eosinofílica e aplasia medular

AU - Falcão, Sandra

AU - Mourão, Ana F.

AU - Ribeiro, Célia

AU - Pinto, Teresa L.

AU - Mateus, Margarida

AU - Araújo, Paula

AU - Nero, Patrícia

AU - Bravo Pimentão, J.

AU - Cunha Branco, J.

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AB - Eosinophilic fasciitis is a rare rheumatic condition characterized by inflammatory thickening of the skin and fascia, peripheral eosinophilia, elevated erythrocyte sedimentation rate and hypergammaglobulinemia. Internal organ involvement is uncommon. It is often difficult to diagnose eosinophilic fasciitis and its course may be variable. Glucocorticoids are most commonly used in the treatment but in many cases they are ineffective, requiring combined immunosuppressive treatment. Several cases of eosinophilic fasciitis and serious haematological disorders such as immune thrombocytopenia, Hodgkin's disease and aplastic anaemia have been described. The authors report an atypical severe case of eosinophilic fasciitis complicated by aplastic anaemia non responsive to treatment.

KW - Aplastic anemia

KW - Eosinophilic fasciitis

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M3 - Article

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AN - SCOPUS:67649690218

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JO - Acta Reumatologica Portuguesa

JF - Acta Reumatologica Portuguesa

IS - 1

ER -

Fasceíte eosinofílica e aplasia medular

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