Ascending aortic dissection associated with primary sarcoma of the aorta. Clinical report

Primary tumors of the aorta are extremely rare and have been associated with aortic dissection, being the intimal sarcoma very aggressive with a propensity to metastasize early. Once the diagnosis has been confirmed, surgical resection may be curative, however the prognosis remains dismal, with death resulting in most patients. We describe a case of type A aortic dissection, with a intramural hematoma, associated with intimal sarcoma, in a young patient, presenting with a cerebral hematoma, ultimately resulting in the patient's death.